Cystic fibrosis. (Q30251439)

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Language	Label	Description	Also known as
English	Cystic fibrosis.	scientific article

Statements

scholarly article

1 reference

Europe PubMed Central

13 June 2017

1 reference

Europe PubMed Central

Cystic fibrosis. (English)

1 reference

Europe PubMed Central

13 June 2017

cystic fibrosis

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object named as

J Stuart Elborn

1

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language of work or name

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publication date

29 April 2016

1 reference

Europe PubMed Central

13 June 2017

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Europe PubMed Central

13 June 2017

388

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Europe PubMed Central

13 June 2017

2519-2531

1 reference

Europe PubMed Central

13 June 2017

10059

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Europe PubMed Central

13 June 2017

CYSTIC FIBROSIS OF THE PANCREAS AND ITS RELATION TO CELIAC DISEASE

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https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Cystic fibrosis since 1938.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Cystic fibrosis: current survival and population estimates to the year 2000.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Future trends in cystic fibrosis demography in 34 European countries

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Antibiotic and anti-inflammatory therapies for cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Managing cystic fibrosis: strategies that increase life expectancy and improve quality of life

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Origins of cystic fibrosis lung disease

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

New pharmacological approaches for cystic fibrosis: promises, progress, pitfalls.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

The prevalence of cystic fibrosis in the European Union

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Consensus on the use and interpretation of cystic fibrosis mutation analysis in clinical practice

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Defining the disease liability of variants in the cystic fibrosis transmembrane conductance regulator gene

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

The relative frequency of CFTR mutation classes in European patients with cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

A new era in the treatment of cystic fibrosis: correction of the underlying CFTR defect.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

PRAGMA-CF. A Quantitative Structural Lung Disease Computed Tomography Outcome in Young Children with Cystic Fibrosis.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Risk Factors for Bronchiectasis in Children with Cystic Fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Early respiratory infection is associated with reduced spirometry in children with cystic fibrosis.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Cystic fibrosis airway secretions exhibit mucin hyperconcentration and increased osmotic pressure

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

A periciliary brush promotes the lung health by separating the mucus layer from airway epithelia

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Bronchiectasis: a continuum of ion transport dysfunction or multiple hits?

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

CFTR and lung homeostasis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Role of epithelial HCO3⁻ transport in mucin secretion: lessons from cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Cystic fibrosis: impaired bicarbonate secretion and mucoviscidosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Impaired mucus detachment disrupts mucociliary transport in a piglet model of cystic fibrosis.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Defective innate immunity and hyperinflammation in newborn cystic fibrosis transmembrane conductance regulator-knockout ferret lungs

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Hypertonic saline is effective in the prevention and treatment of mucus obstruction, but not airway inflammation, in mice with chronic obstructive lung disease

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Cigarette smoke exposure induces CFTR internalization and insolubility, leading to airway surface liquid dehydration

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Acquired defects in CFTR-dependent β-adrenergic sweat secretion in chronic obstructive pulmonary disease

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Cigarette smoke induces systemic defects in cystic fibrosis transmembrane conductance regulator function

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Cigarette smoke and CFTR: implications in the pathogenesis of COPD

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Another Beginning for Cystic Fibrosis Therapy

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Changing epidemiology and clinical issues arising in an ageing cystic fibrosis population

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Comparative demographics of the European cystic fibrosis population: a cross-sectional database analysis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Standards of Care for Cystic Fibrosis ten years later.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

European Cystic Fibrosis Society Standards of Care: Framework for the Cystic Fibrosis Centre

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

European Cystic Fibrosis Society Standards of Care: Best Practice guidelines

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

A European consensus for the evaluation and management of infants with an equivocal diagnosis following newborn screening for cystic fibrosis.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

European best practice guidelines for cystic fibrosis neonatal screening

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Economic implications of newborn screening for cystic fibrosis: a cost of illness retrospective cohort study

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

New challenges in the diagnosis and management of cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Clinical features associated with a delayed diagnosis of cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Correlation of sweat chloride concentration with classes of the cystic fibrosis transmembrane conductance regulator gene mutations

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Modifier genes in Mendelian disorders: the example of cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Genetic modifiers of cystic fibrosis-related diabetes

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Genetic modifiers of liver disease in cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Interpretation of genetic variants

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

CFTR p.Arg117His associated with CBAVD and other CFTR-related disorders

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Association of sweat chloride concentration at time of diagnosis and CFTR genotype with mortality and cystic fibrosis phenotype

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Effects of gender and age at diagnosis on disease progression in long-term survivors of cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

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Cystic fibrosis genetics: from molecular understanding to clinical application

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Cystic fibrosis: a mucosal immunodeficiency syndrome.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

A new player in the game: epithelial cathepsin S in early cystic fibrosis lung disease.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Inflammation in cystic fibrosis lung disease: Pathogenesis and therapy

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Sputum biomarkers of inflammation and lung function decline in children with cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Lack of neutrophil elastase reduces inflammation, mucus hypersecretion, and emphysema, but not mucus obstruction, in mice with cystic fibrosis-like lung disease

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

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Infections in patients with cystic fibrosis: diagnostic microbiology update

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Emerging bacterial pathogens and changing concepts of bacterial pathogenesis in cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

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Cystic fibrosis microbiology: Advances in antimicrobial therapy.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Antimicrobial resistance in the respiratory microbiota of people with cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Whole-genome sequencing to identify transmission of Mycobacterium abscessus between patients with cystic fibrosis: a retrospective cohort study

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

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The growing threat of nontuberculous mycobacteria in CF

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Lung microbiota and bacterial abundance in patients with bronchiectasis when clinically stable and during exacerbation

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

The adult cystic fibrosis airway microbiota is stable over time and infection type, and highly resilient to antibiotic treatment of exacerbations

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Reduced bacterial colony count of anaerobic bacteria is associated with a worsening in lung clearance index and inflammation in cystic fibrosis.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Lung microbiota across age and disease stage in cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Changes in cystic fibrosis airway microbial community associated with a severe decline in lung function

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

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Infection prevention and control guideline for cystic fibrosis: 2013 update

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Epidemiology of infection and current guidelines for infection prevention in cystic fibrosis patients

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Shared Pseudomonas aeruginosa genotypes are common in Australian cystic fibrosis centres

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Viability of Pseudomonas aeruginosa in cough aerosols generated by persons with cystic fibrosis.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Factors influencing acquisition of Burkholderia cepacia complex organisms in patients with cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Airway inflammation in cystic fibrosis: molecular mechanisms and clinical implications

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

The challenges of developing effective anti-inflammatory agents in cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Cystic fibrosis pulmonary guidelines: treatment of pulmonary exacerbations

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Cystic fibrosis pulmonary guidelines. Chronic medications for maintenance of lung health

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Treatment of lung infection in patients with cystic fibrosis: current and future strategies

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Cystic fibrosis research in allied health and nursing professions.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

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Long-term multicentre randomised controlled study of high frequency chest wall oscillation versus positive expiratory pressure mask in cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Prevention of chronic Pseudomonas aeruginosa colonisation in cystic fibrosis by early treatment

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Treatment of early Pseudomonas aeruginosa infection in patients with cystic fibrosis: the ELITE trial

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Comparison of two treatment regimens for eradication of Pseudomonas aeruginosa infection in children with cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Early antibiotic treatment for Pseudomonas aeruginosa eradication in patients with cystic fibrosis: a randomised multicentre study comparing two different protocols.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Cystic Fibrosis Foundation pulmonary guideline. pharmacologic approaches to prevention and eradication of initial Pseudomonas aeruginosa infection

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Indicators of pulmonary exacerbation in cystic fibrosis: A Delphi survey of patients and health professionals.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Systematic review of blood biomarkers in cystic fibrosis pulmonary exacerbations

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Antibiotic management of lung infections in cystic fibrosis. I. The microbiome, methicillin-resistant Staphylococcus aureus, gram-negative bacteria, and multiple infections

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Effect of pulmonary exacerbations on long-term lung function decline in cystic fibrosis.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Exacerbation frequency and clinical outcomes in adult patients with cystic fibrosis.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Animal models of gastrointestinal and liver diseases. Animal models of cystic fibrosis: gastrointestinal, pancreatic, and hepatobiliary disease and pathophysiology.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Cystic fibrosis: An update for clinicians. Part 1: Nutrition and gastrointestinal complications

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Cystic fibrosis and the role of gastrointestinal outcome measures in the new era of therapeutic CFTR modulation

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Cystic fibrosis: an update for clinicians. Part 2: hepatobiliary and pancreatic manifestations

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Resting energy expenditure and oxygen cost of breathing in patients with cystic fibrosis.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Pancreatic enzyme replacement therapy for people with cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Management of comorbidities in older patients with cystic fibrosis.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

New insights into cystic fibrosis-related diabetes in children

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Update on cystic fibrosis-related diabetes

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Cystic fibrosis-related bone disease: insights into a growing problem

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

European cystic fibrosis bone mineralisation guidelines

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Multicentre trial of weekly risedronate on bone density in adults with cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Aminoglycoside use in cystic fibrosis: therapeutic strategies and toxicity.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

End of life care for patients with cystic fibrosis.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Palliative and end-of-life care in cystic fibrosis: what we know and what we need to know

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Lung transplantation for cystic fibrosis and bronchiectasis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Practical guidelines: lung transplantation in patients with cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Development and evaluation of a palliative care curriculum for cystic fibrosis healthcare providers.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Longitudinal trends in health-related quality of life in adults with cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Cystic Fibrosis Foundation and European Cystic Fibrosis Society Survey of cystic fibrosis mental health care delivery.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

International Committee on Mental Health in Cystic Fibrosis: Cystic Fibrosis Foundation and European Cystic Fibrosis Society consensus statements for screening and treating depression and anxiety

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

A systematic review of factors associated with health-related quality of life in adolescents and adults with cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Prevalence of depression and anxiety in patients with cystic fibrosis and parent caregivers: results of The International Depression Epidemiological Study across nine countries

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Rescue of CF airway epithelial cell function in vitro by a CFTR potentiator, VX-770

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Ivacaftor potentiation of multiple CFTR channels with gating mutations

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Effect of ivacaftor on CFTR forms with missense mutations associated with defects in protein processing or function

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

A CFTR potentiator in patients with cystic fibrosis and the G551D mutation

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Efficacy and safety of ivacaftor in patients aged 6 to 11 years with cystic fibrosis with a G551D mutation

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Assessment of clinical response to ivacaftor with lung clearance index in cystic fibrosis patients with a G551D-CFTR mutation and preserved spirometry: a randomised controlled trial

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Long-term safety and efficacy of ivacaftor in patients with cystic fibrosis who have the Gly551Asp-CFTR mutation: a phase 3, open-label extension study (PERSIST).

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Clinical mechanism of the cystic fibrosis transmembrane conductance regulator potentiator ivacaftor in G551D-mediated cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Efficacy and safety of ivacaftor in patients with cystic fibrosis and a non-G551D gating mutation

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Efficacy and safety of ivacaftor in patients with cystic fibrosis who have an Arg117His-CFTR mutation: a double-blind, randomised controlled trial

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Ataluren for the treatment of nonsense-mutation cystic fibrosis: a randomised, double-blind, placebo-controlled phase 3 trial

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Ataluren (PTC124) induces cystic fibrosis transmembrane conductance regulator protein expression and activity in children with nonsense mutation cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Lumacaftor-Ivacaftor in Patients with Cystic Fibrosis Homozygous for Phe508del CFTR.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

A CFTR corrector (lumacaftor) and a CFTR potentiator (ivacaftor) for treatment of patients with cystic fibrosis who have a phe508del CFTR mutation: a phase 2 randomised controlled trial

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Correction of the F508del-CFTR protein processing defect in vitro by the investigational drug VX-809.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Some gating potentiators, including VX-770, diminish ΔF508-CFTR functional expression.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Potentiator ivacaftor abrogates pharmacological correction of ΔF508 CFTR in cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Repeated nebulisation of non-viral CFTR gene therapy in patients with cystic fibrosis: a randomised, double-blind, placebo-controlled, phase 2b trial.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Clinical trials in cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Lung clearance index: evidence for use in clinical trials in cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

CFTR biomarkers: time for promotion to surrogate end-point.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

European Cystic Fibrosis Society Standards of Care: a road map to improve CF outcome

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

European Cystic Fibrosis Society Standards of Care: Quality Management in cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2816%2900576-6

7 January 2021

based on heuristic

inferred from DOI database lookup

Identifiers

10.1016/S0140-6736(16)00576-6

1 reference

Europe PubMed Central

13 June 2017

1 reference

Europe PubMed Central

13 June 2017

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