Functional Rescue of ABCC6 Deficiency by 4-Phenylbutyrate Therapy Reduces Dystrophic Calcification in Abcc6-/- Mice. (Q48939711)

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27 March 2020

title

Functional Rescue of ABCC6 Deficiency by 4-Phenylbutyrate Therapy Reduces Dystrophic Calcification in Abcc6-/- Mice (English)

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27 March 2020

3

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27 March 2020

author name string

Viola Pomozi

1

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27 March 2020

Christopher Brampton

2

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27 March 2020

Dóra Dedinszki

4

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27 March 2020

Eszter Kozák

5

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27 March 2020

Koen van de Wetering

6

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27 March 2020

Hi'ilani Hopkins

7

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27 March 2020

Ludovic Martin

8

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27 March 2020

András Váradi

9

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27 March 2020

Olivier Le Saux

10

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27 March 2020

language of work or name

English

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publication date

5 November 2016

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Journal of Investigative Dermatology

27 March 2020

published in

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27 March 2020

volume

137

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issue

3

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page(s)

595-602

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Successful treatment with 4-phenylbutyrate in a patient with benign recurrent intrahepatic cholestasis type 2 refractory to biliary drainage and bilirubin absorption

27 March 2020

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Identifiers

DOI

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27 March 2020

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27 March 2020

PubMed publication ID

27826008

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