Immune responses in cystic fibrosis: are they intrinsically defective? (Q37992061)

26 August 2017

Immune responses in cystic fibrosis: are they intrinsically defective? (English)

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26 August 2017

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Dmitry Ratner

1

1 reference

PubMed ID

22403802

26 August 2017

Christian Mueller

series ordinal

2

1 reference

26 August 2017

8 March 2012

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American Journal of Respiratory Cell and Molecular Biology

26 August 2017

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26 August 2017

46

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26 August 2017

715-722

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26 August 2017

6

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Exaggerated activation of nuclear factor-kappaB and altered IkappaB-beta processing in cystic fibrosis bronchial epithelial cells

26 August 2017

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Exaggerated apoptosis and NF-kappaB activation in pancreatic and tracheal cystic fibrosis cells.

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Lack of cystic fibrosis transmembrane conductance regulator in CD3+ lymphocytes leads to aberrant cytokine secretion and hyperinflammatory adaptive immune responses

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Patterns of medical practice in cystic fibrosis: part I. Evaluation and monitoring of health status of patients. Investigators and Coordinators of the Epidemiologic Study of Cystic Fibrosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Phacomatosis pigmentokeratotica.

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Cutaneous manifestations of cystic fibrosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Antibiotic hypersensitivity in CF: drug-induced life-threatening hemolytic anemia in a pediatric patient

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Antibiotic allergy in cystic fibrosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Beta-lactam allergy in adults with cystic fibrosis.

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Alveolar inflammation in cystic fibrosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Cytokine secretion by cystic fibrosis airway epithelial cells

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Cystic fibrosis transmembrane conductance regulator does not affect neutrophil migration across cystic fibrosis airway epithelial monolayers

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Interleukin-8 production by cystic fibrosis nasal epithelial cells after tumor necrosis factor-alpha and respiratory syncytial virus stimulation

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Murine models of chronic Pseudomonas aeruginosa lung infection

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Role of Cftr genotype in the response to chronic Pseudomonas aeruginosa lung infection in mice

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Response to acute lung infection with mucoid Pseudomonas aeruginosa in cystic fibrosis mice

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Plasma membrane CFTR regulates RANTES expression via its C-terminal PDZ-interacting motif

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Physiological modulation of CFTR activity by AMP-activated protein kinase in polarized T84 cells

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Regulation of channel gating by AMP-activated protein kinase modulates cystic fibrosis transmembrane conductance regulator activity in lung submucosal cells

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Inhibition of cystic fibrosis transmembrane conductance regulator by novel interaction with the metabolic sensor AMP-activated protein kinase

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Innate inflammatory responses of pediatric cystic fibrosis airway epithelial cells: effects of nonviral and viral stimulation

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

CFTR negatively regulates cyclooxygenase-2-PGE(2) positive feedback loop in inflammation

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Characterization of LPS-induced lung inflammation in cftr-/- mice and the effect of docosahexaenoic acid

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Effects of CFTR, interleukin-10, and Pseudomonas aeruginosa on gene expression profiles in a CF bronchial epithelial cell Line

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Strain-dependent pulmonary gene expression profiles of a cystic fibrosis mouse model

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

A macromolecular complex of beta 2 adrenergic receptor, CFTR, and ezrin/radixin/moesin-binding phosphoprotein 50 is regulated by PKA

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Compartmentalized cyclic adenosine 3',5'-monophosphate at the plasma membrane clusters PDE3A and cystic fibrosis transmembrane conductance regulator into microdomains

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

The functional network of ion channels in T lymphocytes

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Cystic fibrosis transmembrane conductance regulator inverts protein kinase A-mediated regulation of epithelial sodium channel single channel kinetics

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Enhanced Ca2+ entry due to Orai1 plasma membrane insertion increases IL-8 secretion by cystic fibrosis airways

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Role of CFTR expressed by neutrophils in modulating acute lung inflammation and injury in mice

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Reduced iC3b-mediated phagocytotic capacity of pulmonary neutrophils in cystic fibrosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

CFTR Expression in human neutrophils and the phagolysosomal chlorination defect in cystic fibrosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

The role of chloride anion and CFTR in killing of Pseudomonas aeruginosa by normal and CF neutrophils

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

CFTR-mediated halide transport in phagosomes of human neutrophils

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

RNA interference against CFTR affects HL60-derived neutrophil microbicidal function

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Specific resistance to Pseudomonas aeruginosa infection in zebrafish is mediated by the cystic fibrosis transmembrane conductance regulator.

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Activated MCTC mast cells infiltrate diseased lung areas in cystic fibrosis and idiopathic pulmonary fibrosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Platelet activation in cystic fibrosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

The inflammatory role of platelets in cystic fibrosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Neutrophils in cystic fibrosis display a distinct gene expression pattern

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Elevated miR-155 promotes inflammation in cystic fibrosis by driving hyperexpression of interleukin-8

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

CFTR inhibition provokes an inflammatory response associated with an imbalance of the annexin A1 pathway.

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Effect of Pseudomonas infection on weight loss, lung mechanics, and cytokines in mice

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Cystic fibrosis pseudomonas opsonins. Inhibitory nature in an in vitro phagocytic assay

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Proteins of the cystic fibrosis respiratory tract. Fragmented immunoglobulin G opsonic antibody causing defective opsonophagocytosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Dysfunctional CFTR alters the bactericidal activity of human macrophages against Pseudomonas aeruginosa

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Disease-causing mutations in the cystic fibrosis transmembrane conductance regulator determine the functional responses of alveolar macrophages

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Cystic fibrosis transmembrane conductance regulator-independent phagosomal acidification in macrophages

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Enhanced susceptibility to pulmonary infection with Burkholderia cepacia in Cftr(-/-) mice

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Calcium-modulated chloride pathways contribute to chloride flux in murine cystic fibrosis-affected macrophages

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Abnormal trafficking and degradation of TLR4 underlie the elevated inflammatory response in cystic fibrosis.

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Monocytes from cystic fibrosis patients are locked in an LPS tolerance state: down-regulation of TREM-1 as putative underlying mechanism.

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

TREM-1 promotes survival during septic shock in mice.

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Cystic fibrosis, disease severity, and a macrophage migration inhibitory factor polymorphism

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Lymphocyte responsiveness to Pseudomonas aeruginosa in cystic fibrosis: Relationship to status of pulmonary disease in sibling pairs

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Pulmonary T(H)2 response in Pseudomonas aeruginosa-infected patients with cystic fibrosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Enhanced IgE allergic response to Aspergillus fumigatus in CFTR-/- mice.

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Increased sensitivity to IL-4 in cystic fibrosis patients with allergic bronchopulmonary aspergillosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Improved outcome of chronic Pseudomonas aeruginosa lung infection is associated with induction of a Th1-dominated cytokine response

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Hypersusceptibility of cystic fibrosis mice to chronic Pseudomonas aeruginosa oropharyngeal colonization and lung infection

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Hyperproliferation and dysregulation of IL-4 expression in NF-ATp-deficient mice

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

The transcription factor NF-ATc1 regulates lymphocyte proliferation and Th2 cytokine production

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Calcium-activated potassium channels sustain calcium signaling in T lymphocytes. Selective blockers and manipulated channel expression levels

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Ryanodine receptor activation by Ca v 1.2 is involved in dendritic cell major histocompatibility complex class II surface expression

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

Monocytes from children with clinically stable cystic fibrosis show enhanced expression of Toll-like receptor 4

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2011-0399RT

21 January 2018

Identifiers

DOI

10.1165/RCMB.2011-0399RT

1 reference

release_egtswotz3zamjpwfd5fufe6q3m

26 August 2017

1 reference

Fatcat

https://api.fatcat.wiki/v0/release/egtswotz3zamjpwfd5fufe6q3m

mapped directly with Wikidata item

24 November 2022

based on heuristic

PubMed ID

22403802

1 reference

PubMed ID

22403802