A functional anatomic defect of the cystic fibrosis airway (Q34425996)

2 August 2017

A functional anatomic defect of the cystic fibrosis airway (English)

1 reference

2 August 2017

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16

Eric J Sorscher

1 reference

2 August 2017

8

Marina Mazur

1 reference

2 August 2017

6

Eric J Wilsterman

1 reference

2 August 2017

Susan E Birket

1

1 reference

2 August 2017

Kengyeh K Chu

2

1 reference

2 August 2017

Linbo Liu

3

1 reference

2 August 2017

Grace H Houser

4

1 reference

2 August 2017

Bradford J Diephuis

5

1 reference

2 August 2017

Gregory Dierksen

7

1 reference

2 August 2017

Suresh Shastry

9

1 reference

2 August 2017

Yao Li

10

1 reference

2 August 2017

John D Watson

11

1 reference

2 August 2017

Alexander T Smith

12

1 reference

2 August 2017

Benjamin S Schuster

13

1 reference

2 August 2017

Justin Hanes

14

1 reference

2 August 2017

William E Grizzle

15

1 reference

2 August 2017

Guillermo J Tearney

17

1 reference

2 August 2017

Steven M Rowe

18

1 reference

2 August 2017

language of work or name

English

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publication date

1 August 2014

1 reference

American Journal of Respiratory and Critical Care Medicine

2 August 2017

1 reference

2 August 2017

190

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2 August 2017

4

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2 August 2017

421-432

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Characterization of defects in ion transport and tissue development in cystic fibrosis transmembrane conductance regulator (CFTR)-knockout rats

2 August 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4214131

Neonates with cystic fibrosis have a reduced nasal liquid pH; a small pilot study

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4214131

Native small airways secrete bicarbonate

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4214131

Cigarette smoke induces systemic defects in cystic fibrosis transmembrane conductance regulator function

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4214131

Intestinal CFTR expression alleviates meconium ileus in cystic fibrosis pigs

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4214131

Method for quantitative study of airway functional microanatomy using micro-optical coherence tomography

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4214131

Mucociliary transport in porcine trachea: differential effects of inhibiting chloride and bicarbonate secretion

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4214131

A pharmacologic approach to acquired cystic fibrosis transmembrane conductance regulator dysfunction in smoking related lung disease

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4214131

Reduced airway surface pH impairs bacterial killing in the porcine cystic fibrosis lung

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4214131

Bicarbonate and functional CFTR channel are required for proper mucin secretion and link cystic fibrosis with its mucus phenotype.

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4214131

Imaging the subcellular structure of human coronary atherosclerosis using micro-optical coherence tomography

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4214131

Human cystic fibrosis airway epithelia have reduced Cl- conductance but not increased Na+ conductance.

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4214131

Use of primary cultures of human bronchial epithelial cells isolated from cystic fibrosis patients for the pre-clinical testing of CFTR modulators

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4214131

Hyperviscous airway periciliary and mucous liquid layers in cystic fibrosis measured by confocal fluorescence photobleaching

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4214131

The ΔF508 mutation causes CFTR misprocessing and cystic fibrosis-like disease in pigs

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4214131

Anion secretion by a model epithelium: more lessons from Calu-3.

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4214131

Measurement of the airway surface liquid volume with simple light refraction microscopy

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4214131

Loss of anion transport without increased sodium absorption characterizes newborn porcine cystic fibrosis airway epithelia

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4214131

Role of epithelial HCO3⁻ transport in mucin secretion: lessons from cystic fibrosis

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4214131

Decreased soluble adenylyl cyclase activity in cystic fibrosis is related to defective apical bicarbonate exchange and affects ciliary beat frequency regulation

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4214131

Cystic fibrosis pigs develop lung disease and exhibit defective bacterial eradication at birth

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4214131

Rescue of CF airway epithelial cell function in vitro by a CFTR potentiator, VX-770

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4214131

Airway surface liquid depth measured in ex vivo fragments of pig and human trachea: dependence on Na+ and Cl- channel function

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4214131

Normal mouse intestinal mucus release requires cystic fibrosis transmembrane regulator-dependent bicarbonate secretion

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4214131

CFTR delivery to 25% of surface epithelial cells restores normal rates of mucus transport to human cystic fibrosis airway epithelium

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4214131

Disruption of the CFTR gene produces a model of cystic fibrosis in newborn pigs

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4214131

Cystic fibrosis: impaired bicarbonate secretion and mucoviscidosis

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4214131

Regulation of normal and cystic fibrosis airway surface liquid volume by phasic shear stress

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4214131

Regulation of airway surface liquid volume and mucus transport by active ion transport

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4214131

Normal and cystic fibrosis airway surface liquid homeostasis. The effects of phasic shear stress and viral infections

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4214131

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4214131

Real-time multiple-particle tracking: applications to drug and gene delivery

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4214131

Mucus secretion from single submucosal glands of pig. Stimulation by carbachol and vasoactive intestinal peptide

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4214131

Submucosal gland secretions in airways from cystic fibrosis patients have normal [Na(+)] and pH but elevated viscosity

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4214131

Noninvasive in vivo fluorescence measurement of airway-surface liquid depth, salt concentration, and pH.

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4214131

Evidence for periciliary liquid layer depletion, not abnormal ion composition, in the pathogenesis of cystic fibrosis airways disease

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4214131

Coordinated clearance of periciliary liquid and mucus from airway surfaces.

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4214131

Human airway ion transport. Part two.

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4214131

Bicarbonate conductance and pH regulatory capability of cystic fibrosis transmembrane conductance regulator

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4214131

Nasal mucociliary clearance and ciliary beat frequency in cystic fibrosis compared with sinusitis and bronchiectasis

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4214131

Effect of viscosity on bacterial motility

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4214131

Missing Cl conductance in cystic fibrosis

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4214131

An apical-membrane chloride channel in human tracheal epithelium

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4214131

Absent secretion to vasoactive intestinal peptide in cystic fibrosis airway glands

6 July 2018

1 reference

https://api.crossref.org/works/10.1164%2FRCCM.201404-0670OC

Mucus properties in children with primary ciliary dyskinesia: comparison with cystic fibrosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FRCCM.201404-0670OC

Liquid secretion inhibitors reduce mucociliary transport in glandular airways

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FRCCM.201404-0670OC

Cystic fibrosis salt/fluid controversy: in the thick of it.

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FRCCM.201404-0670OC

A controlled trial of long-term inhaled hypertonic saline in patients with cystic fibrosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FRCCM.201404-0670OC

Mucus clearance and lung function in cystic fibrosis with hypertonic saline

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FRCCM.201404-0670OC

Long-term inhaled dry powder mannitol in cystic fibrosis: an international randomized study.

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FRCCM.201404-0670OC

Role of the amiloride-sensitive epithelial Na+ channel in the pathogenesis and as a therapeutic target for cystic fibrosis lung disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FRCCM.201404-0670OC

Evaluation of the intestinal current measurement method as a diagnostic test for cystic fibrosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FRCCM.201404-0670OC

Effect of anion transport inhibition on mucus secretion by airway submucosal glands

21 January 2018

1 reference

PubMed

https://pubmed.ncbi.nlm.nih.gov/25029666

inferred from PubMed ID database lookup

12 December 2020

based on heuristic

CFTR involvement in chloride, bicarbonate, and liquid secretion by airway submucosal glands

1 reference

PubMed

https://pubmed.ncbi.nlm.nih.gov/25029666

inferred from PubMed ID database lookup

12 December 2020

based on heuristic

Identifiers

DOI

10.1164/RCCM.201404-0670OC

1 reference

2 August 2017

1 reference

2 August 2017

1 reference