Loss of anion transport without increased sodium absorption characterizes newborn porcine cystic fibrosis airway epithelia (Q34671320)

3 August 2017

Loss of anion transport without increased sodium absorption characterizes newborn porcine cystic fibrosis airway epithelia (English)

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3 August 2017

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8

Leah R Reznikov

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3 August 2017

Jeng-Haur Chen

1

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3 August 2017

David A Stoltz

2

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3 August 2017

Philip H Karp

3

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3 August 2017

Sarah E Ernst

4

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3 August 2017

Alejandro A Pezzulo

5

1 reference

3 August 2017

Thomas O Moninger

6

1 reference

3 August 2017

Michael V Rector

7

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3 August 2017

Janice L Launspach

9

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3 August 2017

Kathryn Chaloner

10

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3 August 2017

Joseph Zabner

11

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3 August 2017

Michael J Welsh

12

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3 August 2017

language of work or name

English

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publication date

1 December 2010

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3 August 2017

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3 August 2017

143

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911-923

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6

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describes a project that uses

3 August 2017

ImageJ

1 reference

11 June 2022

https://www.ebi.ac.uk/europepmc/webservices/rest/PMC3057187/fullTextXML

inferred from PubMed Central ID database lookup

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7 July 2018

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ENaC-CFTR interactions: the role of electrical coupling of ion fluxes explored in an epithelial cell model

7 July 2018

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7 July 2018

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Evidence for periciliary liquid layer depletion, not abnormal ion composition, in the pathogenesis of cystic fibrosis airways disease

7 July 2018

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The amiloride-inhibitable Na+ conductance is reduced by the cystic fibrosis transmembrane conductance regulator in normal but not in cystic fibrosis airways.

7 July 2018

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7 July 2018

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Relationship of a non-cystic fibrosis transmembrane conductance regulator-mediated chloride conductance to organ-level disease in Cftr(-/-) mice

7 July 2018

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7 July 2018

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7 July 2018

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7 July 2018

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7 July 2018

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Sodium transport and intracellular sodium activity in cultured human nasal epithelium.

7 July 2018

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An analytical model of ionic movements in airway epithelial cells

7 July 2018

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cAMP stimulates bicarbonate secretion across normal, but not cystic fibrosis airway epithelia

7 July 2018

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Quantification of periciliary fluid height in human airway biopsies is feasible, but not suitable as a biomarker

7 July 2018

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Functional characterization of a partial loss-of-function mutation of the epithelial sodium channel (ENaC) associated with atypical cystic fibrosis.

26 October 2018

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Mutations in the amiloride-sensitive epithelial sodium channel in patients with cystic fibrosis-like disease.

26 October 2018

1 reference

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Airway surface liquid volume regulates ENaC by altering the serine protease-protease inhibitor balance: a mechanism for sodium hyperabsorption in cystic fibrosis.

26 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3057187

Mucus clearance and lung function in cystic fibrosis with hypertonic saline

26 October 2018

1 reference

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A controlled trial of long-term inhaled hypertonic saline in patients with cystic fibrosis

26 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3057187

Flagellin of Pseudomonas aeruginosa inhibits Na+ transport in airway epithelia

26 October 2018

1 reference

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Hyposecretion, not hyperabsorption, is the basic defect of cystic fibrosis airway glands

26 October 2018

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https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3057187

Mutations in the beta-subunit of the epithelial Na+ channel in patients with a cystic fibrosis-like syndrome

26 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3057187

Regulation of MUC5AC mucin secretion and airway surface liquid metabolism by IL-1β in human bronchial epithelia

26 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3057187

An in vitro model of differentiated human airway epithelia. Methods for establishing primary cultures.

26 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3057187

Pulmonary epithelial sodium-channel dysfunction and excess airway liquid in pseudohypoaldosteronism

26 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3057187

Physiological basis of cystic fibrosis: a historical perspective

26 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3057187

Loss of CFTR chloride channels alters salt absorption by cystic fibrosis airway epithelia in vitro.

26 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3057187

Edge damage effect on electrical measurements of frog skin

26 October 2018

1 reference

PubMed

https://pubmed.ncbi.nlm.nih.gov/21145458

12 December 2020

inferred from PubMed ID database lookup

Increased bioelectric potential difference across respiratory epithelia in cystic fibrosis

1 reference

PubMed

https://pubmed.ncbi.nlm.nih.gov/21145458

12 December 2020

inferred from PubMed ID database lookup

Abnormal Ion Permeation Through Cystic Fibrosis Respiratory Epithelium

1 reference

PubMed

https://pubmed.ncbi.nlm.nih.gov/21145458

12 December 2020

inferred from PubMed ID database lookup

Identifiers

DOI

10.1016/J.CELL.2010.11.029

1 reference

3 August 2017

1 reference

3 August 2017

1 reference