Defective CFTR expression and function are detectable in blood monocytes: development of a new blood test for cystic fibrosis (Q28479231)

2

0 references

Claudio Sorio

object named as

Claudio Sorio

1

0 references

Jan Johansson

5

object named as

Jan Johansson

0 references

author name string

Chiara Angiari

3

0 references

Michele Ettorre

4

0 references

Marzia Vezzalini

6

0 references

Laura Viviani

7

0 references

Genny Verzè

9

0 references

Baroukh Maurice Assael

10

0 references

Paola Melotti

Creative Commons Attribution 4.0 International

11

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language of work or name

English

0 references

publication date

2011

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published in

PLOS One

0 references

volume

6

0 references

issue

7

0 references

page(s)

e22212

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copyright license

start time

21 July 2011

1 reference

April 2022 Public Data File from Crossref

copyright status

copyrighted

0 references

cites work

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CFTR function and prospects for therapy

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CFTR Expression in human neutrophils and the phagolysosomal chlorination defect in cystic fibrosis

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29 September 2017

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Human epithelial cystic fibrosis transmembrane conductance regulator without exon 5 maintains partial chloride channel function in intracellular membranes

29 September 2017

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CFTR chloride channels in human and simian heart

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Regulation of transepithelial ion transport and intracellular calcium by extracellular ATP in human normal and cystic fibrosis airway epithelium

29 September 2017

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Expression of the cystic fibrosis transmembrane conductance regulator gene in cells of non-epithelial origin

29 September 2017

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A cystic fibrosis pancreatic adenocarcinoma cell line

29 September 2017

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Human lymphocytes transcribe the cystic fibrosis transmembrane conductance regulator gene and exhibit CF-defective cAMP-regulated chloride current

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Establishment and characterization of a human pancreatic cancer cell line (SUIT-2) producing carcinoembryonic antigen and carbohydrate antigen 19-9.

2 June 2018

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2 June 2018

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A Cystic Fibrosis Bronchial Epithelial Cell Line: Immortalization by Adeno-12-SV40 Infection

2 June 2018

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Alterations in ceramide concentration and pH determine the release of reactive oxygen species by Cftr-deficient macrophages on infection

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Effectiveness of PTC124 treatment of cystic fibrosis caused by nonsense mutations: a prospective phase II trial

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Macrophages directly contribute to the exaggerated inflammatory response in cystic fibrosis transmembrane conductance regulator-/- mice

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Normal sweat chloride values do not exclude the diagnosis of cystic fibrosis

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12 December 2020

The molecular basis of disease variability among cystic fibrosis patients carrying the 3849+10 kb C-->T mutation

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CFTR regulates phagosome acidification in macrophages and alters bactericidal activity

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Editorial: The role of macrophages and their scavenger receptors in cystic fibrosis

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Clinical Phenotype and Genotype of Children with Borderline Sweat Test and Abnormal Nasal Epithelial Chloride Transport

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