Batten's disease: clues to neuronal protein catabolism in lysosomes (Q22253405)

CLN5 intracellular trafficking protein

Europe PubMed Central

title

Batten's disease: clues to neuronal protein catabolism in lysosomes (English)

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main subject

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CLN6 transmembrane ER protein

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Palmitoyl-protein thioesterase 1

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CLN8 transmembrane ER and ERGIC protein

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tripeptidyl peptidase 1

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protein catabolic process

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Journal of Neuroscience Research

G Dawson

1

G

Dawson

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28 March 2023

S Cho

series ordinal

2

author given names

S

author last names

Cho

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28 March 2023

language of work or name

English

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publication date

15 April 2000

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published in

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volume

60

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page(s)

133-40

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issue

2

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cites work

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7 January 2021

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7 January 2021

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7 January 2021

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7 January 2021

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7 January 2021

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7 January 2021

Specific delay in the degradation of mitochondrial ATP synthase subunit c in late infantile neuronal ceroid lipofuscinosis is derived from cellular proteolytic dysfunction rather than structural alteration of subunit c

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7 January 2021

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7 January 2021

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7 January 2021

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7 January 2021

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7 January 2021

The neuronal ceroid-lipofuscinoses

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7 January 2021