Metabolism of methylmalonic acid in rats. Is methylmalonyl-coenzyme a racemase deficiency symptomatic in man? (Q40984473)

25 September 2017

Metabolism of methylmalonic acid in rats. Is methylmalonyl-coenzyme a racemase deficiency symptomatic in man? (English)

1 reference

25 September 2017

3

Scriver CR

1 reference

25 September 2017

Montgomery JA

1

1 reference

PMCID

437034

25 September 2017

Mamer OA

series ordinal

2

1 reference

PMCID

437034

25 September 2017

language of work or name

English

0 references

publication date

1 December 1983

1 reference

Journal of Clinical Investigation

25 September 2017

1 reference

25 September 2017

72

1 reference

25 September 2017

1937-1947

1 reference

25 September 2017

6

1 reference

On the mechanism of the rearrangement of methylmalonyl-Co A into succinyl-Co A. II. Experiments on the mechanism of action of methylmalonyl-Co A isomerase and methylmalonyl-Co A racemase

25 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=437034

Metabolism of propionic acid in animal tissues. IX. Methylmalonyl coenzyme A racemase

25 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=437034

Metabolism of propionic acid in animal tissues. VIII. Crystalline propionyl carboxylase

25 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=437034

13CValine metabolism in methylmalonicacidemia using nuclear magnetic resonance: propinonate as an obligate intermediate

25 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=437034

Demonstration of a new mammalian isoleucine catabolic pathway yielding an Rseries of metabolites

25 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=437034

Investigation of the Mechanism of the Methylmalonyl-CoA Mutase Reaction with the Substrate Analogue: Ethylmalonyl-CoA

25 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=437034

Methylmalonyl coenzyme A racemase defect: another cause of methylmalonic aciduria.

25 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=437034

Effect of vitamin B12 deprivation on the in vivo levels of coenzyme A intermediates associated with propionate metabolism.

17 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=437034

Metabolism in rats in vivo of RS-2-methylbutyrate and n-butyrate labeled with stable isotopes at various positions. Mechanism of biosynthesis and degradation of ethylmalonyl semialdehyde and ethylmalonic acid

17 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=437034

The absolute configuration of methylmalonyl-CoA

17 June 2018

1 reference

12 December 2020

METABOLISM OF PROPIONIC ACID IN ANIMAL TISSUES. XI. FURTHER STUDIES ON CRYSTALLINE PROPIONYL COENZYME A CARBOXYLASE

1 reference

12 December 2020

A rapid method for the analysis of urinary methylmalonic acid

1 reference

12 December 2020

Metabolism in rats in vivo of isobutyrates labeled with stable isotopes at various positions. Identification of propionate as an obligate intermediate

1 reference

12 December 2020

Improved prenatal diagnosis of methylmalonic acidemia: mass fragmentography of methylmalonic acid in amniotic fluid and maternal urine

1 reference

12 December 2020

Isotope studies on the metabolism of valine

1 reference

12 December 2020

Coenzyme A thiol esters of isobutyric, methacrylic, and beta-hydroxyisobutyric acids as intermediates in the enzymatic degradation of valine

1 reference

12 December 2020

Studies on methylmalonyl isomerase

1 reference

12 December 2020

Studies on the mechanism of fatty acid synthesis. XII. Acetyl coenzyme A carboxylase

1 reference

12 December 2020

Mechanism of action of coenzyme B12. Hydrogen transfer in the isomerization of methylmalonyl coenzyme A to succinyl coenzyme A

1 reference

12 December 2020

Identifiers

DOI

10.1172/JCI111158

1 reference

25 September 2017

1 reference

25 September 2017

1 reference

PMCID

437034