Intracellular aggregation of human stefin B: confocal and electron microscopy study. (Q39751498)

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16 January 2020

title

Intracellular aggregation of human stefin B: confocal and electron microscopy study (English)

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16 January 2020

2

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author name string

Slavko Ceru

1

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16 January 2020

Tina Zavasnik-Bergant

3

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Urska Repnik

4

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16 January 2020

Natasa Kopitar-Jerala

5

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16 January 2020

Vito Turk

6

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16 January 2020

Eva Zerovnik

7

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16 January 2020

publication date

17 March 2010

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16 January 2020

number of pages

16

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based on heuristic

inferred from page(s)

published in

Biology of the Cell

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volume

102

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issue

6

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page(s)

319-334

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Loss of lysosomal association of cystatin B proteins representing progressive myoclonus epilepsy, EPM1, mutations.

16 January 2020

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Interaction of human stefin B in the prefibrillar oligomeric form with membranes. Correlation with cellular toxicity

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Aggresomes do not represent a general cellular response to protein misfolding in mammalian cells

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Cystatin B and its EPM1 mutants are polymeric and aggregate prone in vivo.

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Selective disruption of lysosomes in HeLa cells triggers apoptosis mediated by cleavage of Bid by multiple papain-like lysosomal cathepsins

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Size and morphology of toxic oligomers of amyloidogenic proteins: a case study of human stefin B.

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New insights into the molecular basis of progressive myoclonus epilepsy: a multiprotein complex with cystatin B.

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Disruption of Axonal Transport by Loss of Huntingtin or Expression of Pathogenic PolyQ Proteins in Drosophila

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Cathepsin B but not cathepsins L or S contributes to the pathogenesis of Unverricht-Lundborg progressive myoclonus epilepsy (EPM1)

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Different propensity to form amyloid fibrils by two homologous proteins-Human stefins A and B: searching for an explanation.

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Essential role of proline isomerization in stefin B tetramer formation

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The channel hypothesis of Alzheimer's disease: current status

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21 January 2018

Identifiers

DOI

10.1042/BC20090163

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:20078424%20AND%20SRC:MED&resulttype=core&format=json

16 January 2020

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