Long-QT syndrome-related sodium channel mutations probed by the dynamic action potential clamp technique. (Q39734591)

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8 January 2020

title

Long-QT syndrome-related sodium channel mutations probed by the dynamic action potential clamp technique (English)

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8 January 2020

4

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8 January 2020

author name string

Géza Berecki

1

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8 January 2020

Jan G Zegers

2

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8 January 2020

Zahurul A Bhuiyan

3

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8 January 2020

Ronald Wilders

5

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8 January 2020

Antoni C G van Ginneken

6

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language of work or name

English

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publication date

27 October 2005

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8 January 2020

published in

Journal of Physiology

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8 January 2020

volume

570

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8 January 2020

issue

Pt 2

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8 January 2020

page(s)

237-250

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Substitution of a conserved alanine in the domain IIIS4-S5 linker of the cardiac sodium channel causes long QT syndrome

8 January 2020

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15 September 2018

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15 September 2018

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A novel SCN5A mutation associated with long QT-3: altered inactivation kinetics and channel dysfunction.

15 September 2018

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Rate-dependent QT shortening mechanism for the LQT3 deltaKPQ mutant

15 September 2018

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De novo mutation in the SCN5A gene associated with early onset of sudden infant death

15 September 2018

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Abrupt rate accelerations or premature beats cause life-threatening arrhythmias in mice with long-QT3 syndrome.

15 September 2018

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Genotype-phenotype correlation in the long-QT syndrome: gene-specific triggers for life-threatening arrhythmias.

15 September 2018

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Enhanced Na(+) channel intermediate inactivation in Brugada syndrome

15 September 2018

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The pause that refreshes, or does it? Mechanisms in torsades de pointes

15 September 2018

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Arrhythmias in the congenital long QT syndrome: how often is torsade de pointes pause dependent?

15 September 2018

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From ionic currents to molecular mechanisms: the structure and function of voltage-gated sodium channels

15 September 2018

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15 September 2018

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15 September 2018

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15 September 2018

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15 September 2018

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Identifiers

DOI

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8 January 2020

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