Exclusive skeletal muscle correction does not modulate dystrophic heart disease in the aged mdx model of Duchenne cardiomyopathy (Q36908212)

17 August 2017

Exclusive skeletal muscle correction does not modulate dystrophic heart disease in the aged mdx model of Duchenne cardiomyopathy (English)

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17 August 2017

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Nalinda B Wasala

1

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17 August 2017

Brian Bostick

series ordinal

2

1 reference

17 August 2017

Yongping Yue

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3

1 reference

17 August 2017

Dongsheng Duan

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4

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17 August 2017

3 March 2013

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17 August 2017

Human Molecular Genetics

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17 August 2017

22

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17 August 2017

13

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17 August 2017

2634-2641

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describes a project that uses

17 August 2017

ImageJ

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11 June 2022

https://www.ebi.ac.uk/europepmc/webservices/rest/PMC3674804/fullTextXML

inferred from PubMed Central ID database lookup

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Microdystrophin ameliorates muscular dystrophy in the canine model of duchenne muscular dystrophy

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Truncated dystrophins reduce muscle stiffness in the extensor digitorum longus muscle of mdx mice.

29 September 2017

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AAV micro-dystrophin gene therapy alleviates stress-induced cardiac death but not myocardial fibrosis in >21-m-old mdx mice, an end-stage model of Duchenne muscular dystrophy cardiomyopathy.

29 September 2017

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Antisense oligonucleotide-mediated exon skipping for Duchenne muscular dystrophy: progress and challenges

29 September 2017

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The absence of dystrophin brain isoform expression in healthy human heart ventricles explains the pathogenesis of 5' X-linked dilated cardiomyopathy.

29 September 2017

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Progress in gene therapy of dystrophic heart disease

29 September 2017

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AAV-microdystrophin therapy improves cardiac performance in aged female mdx mice.

29 September 2017

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Pip5 transduction peptides direct high efficiency oligonucleotide-mediated dystrophin exon skipping in heart and phenotypic correction in mdx mice.

29 September 2017

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Phenotyping cardiac gene therapy in mice

29 September 2017

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Nitrosative stress elicited by nNOSµ delocalization inhibits muscle force in dystrophin-null mice

29 September 2017

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Gender influences cardiac function in the mdx model of Duchenne cardiomyopathy.

29 September 2017

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Alterations in mitochondrial function as a harbinger of cardiomyopathy: lessons from the dystrophic heart

29 September 2017

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Current understanding and management of dilated cardiomyopathy in Duchenne and Becker muscular dystrophy.

29 September 2017

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Sub-physiological sarcoglycan expression contributes to compensatory muscle protection in mdx mice

29 September 2017

1 reference

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Cardiac expression of a mini-dystrophin that normalizes skeletal muscle force only partially restores heart function in aged Mdx mice.

29 September 2017

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A single intravenous injection of adeno-associated virus serotype-9 leads to whole body skeletal muscle transduction in dogs.

29 September 2017

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Consequences of disrupting the dystrophin-sarcoglycan complex in cardiac and skeletal myopathy

29 September 2017

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Challenges and opportunities in dystrophin-deficient cardiomyopathy gene therapy.

29 September 2017

1 reference

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Multiple pathogenetic mechanisms in X linked dilated cardiomyopathy

29 September 2017

1 reference

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Full-length dystrophin expression in half of the heart cells ameliorates beta-isoproterenol-induced cardiomyopathy in mdx mice

29 September 2017

1 reference

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Severe cardiomyopathy in mice lacking dystrophin and MyoD

29 September 2017

1 reference

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Expression of full-length utrophin prevents muscular dystrophy in mdx mice

29 September 2017

1 reference

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Emergent dilated cardiomyopathy caused by targeted repair of dystrophic skeletal muscle

29 September 2017

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Pip6-PMO, A New Generation of Peptide-oligonucleotide Conjugates With Improved Cardiac Exon Skipping Activity for DMD Treatment.

29 September 2017

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Interplay between heart and skeletal muscle disease in heart failure: the 2011 George E. Brown Memorial Lecture

27 June 2018

1 reference

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Dystrophies and heart disease.

27 June 2018

1 reference

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The incidence and evolution of cardiomyopathy in Duchenne muscular dystrophy

27 June 2018

1 reference

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Long-term systemic administration of unconjugated morpholino oligomers for therapeutic expression of dystrophin by exon skipping in skeletal muscle: implications for cardiac muscle integrity

27 June 2018

1 reference

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Programmed electrical stimulation in mice

4 September 2018

1 reference

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Effects of exercise training on myocardial energy metabolism and ventricular function assessed by quantitative phosphorus-31 magnetic resonance spectroscopy and magnetic resonance imaging in dilated cardiomyopathy

4 September 2018

1 reference

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Prevention of dystrophin-deficient cardiomyopathy in twenty-one-month-old carrier mice by mosaic dystrophin expression or complementary dystrophin/utrophin expression

4 September 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3674804

Dystrophin-deficient mdx mice display a reduced life span and are susceptible to spontaneous rhabdomyosarcoma.

4 September 2018

1 reference

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Cardiovascular health supervision for individuals affected by Duchenne or Becker muscular dystrophy

4 September 2018

1 reference

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Dystrophic heart failure blocked by membrane sealant poloxamer

4 September 2018

1 reference

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Rapid progression from hypertrophic cardiomyopathy to heart failure in a patient with Becker's muscular dystrophy.

4 September 2018

1 reference

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Modular flexibility of dystrophin: implications for gene therapy of Duchenne muscular dystrophy

4 September 2018

1 reference

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Measurement of heart rate and Q-T interval in the conscious mouse.

4 September 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3674804

Brief report: deletion of the dystrophin muscle-promoter region associated with X-linked dilated cardiomyopathy.

4 September 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3674804

Treatment of the heart in Duchenne muscular dystrophy

4 September 2018

1 reference

12 December 2020

Systemic administration of micro-dystrophin restores cardiac geometry and prevents dobutamine-induced cardiac pump failure

1 reference

12 December 2020

Diaphragm rescue alone prevents heart dysfunction in dystrophic mice

1 reference

12 December 2020

X-linked dilated cardiomyopathy. Molecular genetic evidence of linkage to the Duchenne muscular dystrophy (dystrophin) gene at the Xp21 locus

1 reference

12 December 2020

Cardiomyopathy is independent of skeletal muscle disease in muscular dystrophy

1 reference

12 December 2020

Identifiers

DOI

10.1093/HMG/DDT112

1 reference

17 August 2017

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17 August 2017

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