Chemical rescue of deltaF508-CFTR mimics genetic repair in cystic fibrosis bronchial epithelial cells. (Q36713641)

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:18285607%20AND%20SRC:MED&resulttype=core&format=json

3 January 2020

title

Chemical rescue of deltaF508-CFTR mimics genetic repair in cystic fibrosis bronchial epithelial cells (English)

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3 January 2020

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3

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3 January 2020

author name string

Om V Singh

series ordinal

1

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3 January 2020

Harvey B Pollard

series ordinal

2

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publication date

19 February 2008

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Molecular & Cellular Proteomics

3 January 2020

published in

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3 January 2020

volume

7

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3 January 2020

issue

6

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3 January 2020

page(s)

1099-1110

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VCP/p97 AAA-ATPase does not interact with the endogenous wild-type cystic fibrosis transmembrane conductance regulator

3 January 2020

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Gene expression profile analysis of 4-phenylbutyrate treatment of IB3-1 bronchial epithelial cell line demonstrates a major influence on heat-shock proteins

30 September 2017

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30 September 2017

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30 September 2017

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DeltaF508-CFTR causes constitutive NF-kappaB activation through an ER-overload response in cystic fibrosis lungs

30 September 2017

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30 September 2017

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HSP70 as endogenous stimulus of the Toll/interleukin-1 receptor signal pathway

30 September 2017

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Induction of HSP70 promotes DeltaF508 CFTR trafficking

30 September 2017

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30 September 2017

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The Hsc70 co-chaperone CHIP targets immature CFTR for proteasomal degradation

30 September 2017

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30 September 2017

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The Hdj-2/Hsc70 chaperone pair facilitates early steps in CFTR biogenesis

30 September 2017

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30 September 2017

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30 September 2017

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In vitro pharmacologic restoration of CFTR-mediated chloride transport with sodium 4-phenylbutyrate in cystic fibrosis epithelial cells containing delta F508-CFTR.

30 September 2017

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30 September 2017

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30 September 2017

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30 September 2017

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30 September 2017

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30 September 2017

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30 September 2017

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30 September 2017

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28 June 2018

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CFTR and outward rectifying chloride channels are distinct proteins with a regulatory relationship

28 June 2018

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28 June 2018

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A Cystic Fibrosis Bronchial Epithelial Cell Line: Immortalization by Adeno-12-SV40 Infection

28 June 2018

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Effect of GRP75/mthsp70/PBP74/mortalin overexpression on intracellular ATP level, mitochondrial membrane potential and ROS accumulation following glucose deprivation in PC12 cells

28 June 2018

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5 September 2018

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5 September 2018

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5 September 2018

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5 September 2018

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5 September 2018

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12 December 2020

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12 December 2020

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12 December 2020

A pilot clinical trial of oral sodium 4-phenylbutyrate (Buphenyl) in deltaF508-homozygous cystic fibrosis patients: partial restoration of nasal epithelial CFTR function

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12 December 2020

Polypeptide flux through bacterial Hsp70: DnaK cooperates with trigger factor in chaperoning nascent chains

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12 December 2020

10.1074/MCP.M700303-MCP200

Identifiers

DOI

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3 January 2020

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3 January 2020

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