Sequestration of mutated alpha1-antitrypsin into inclusion bodies is a cell-protective mechanism to maintain endoplasmic reticulum function. (Q36438832)

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:18045994%20AND%20SRC:MED&resulttype=core&format=json

28 December 2019

title

Sequestration of mutated alpha1-antitrypsin into inclusion bodies is a cell-protective mechanism to maintain endoplasmic reticulum function (English)

1 reference

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28 December 2019

main subject

endoplasmic reticulum

0 references

author

Vanessa Nicolin

4

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28 December 2019

author name string

Susana Granell

1

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28 December 2019

Giovanna Baldini

2

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28 December 2019

Sameer Mohammad

3

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28 December 2019

Paola Narducci

5

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28 December 2019

Brian Storrie

6

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28 December 2019

Giulia Baldini

7

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28 December 2019

publication date

28 November 2007

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Molecular Biology of the Cell

28 December 2019

published in

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28 December 2019

volume

19

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28 December 2019

issue

2

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28 December 2019

page(s)

572-586

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EDEM1 reveals a quality control vesicular transport pathway out of the endoplasmic reticulum not involving the COPII exit sites

28 December 2019

cites work

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Grp78, Grp94, and Grp170 interact with alpha1-antitrypsin mutants that are retained in the endoplasmic reticulum

30 September 2017

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30 September 2017

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Inclusion body formation reduces levels of mutant huntingtin and the risk of neuronal death

30 September 2017

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Mutants of neuroserpin that cause dementia accumulate as polymers within the endoplasmic reticulum

30 September 2017

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30 September 2017

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Frame switch splicing and regulated intramembrane proteolysis: key words to understand the unfolded protein response

30 September 2017

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EDEM as an acceptor of terminally misfolded glycoproteins released from calnexin

30 September 2017

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30 September 2017

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30 September 2017

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30 September 2017

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30 September 2017

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30 September 2017

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30 September 2017

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30 September 2017

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30 September 2017

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30 September 2017

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30 September 2017

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30 September 2017

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30 September 2017

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30 September 2017

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30 September 2017

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30 September 2017

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30 September 2017

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30 September 2017

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30 September 2017

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30 September 2017

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30 September 2017

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28 June 2018

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28 June 2018

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21 September 2018

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21 September 2018

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Molecular mousetraps and the serpinopathies

21 September 2018

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Misfolded proinsulin accumulates in expanded pre-Golgi intermediates and endoplasmic reticulum subdomains in pancreatic beta cells of Akita mice

21 September 2018

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Mitochondrial autophagy and injury in the liver in alpha 1-antitrypsin deficiency.

21 September 2018

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21 September 2018

Conformational disease

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21 September 2018

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Processing by endoplasmic reticulum mannosidases partitions a secretion-impaired glycoprotein into distinct disposal pathways

21 September 2018

1 reference

12 December 2020

Retention of mutant alpha(1)-antitrypsin Z in endoplasmic reticulum is associated with an autophagic response

1 reference

12 December 2020

Rab3A and Rab3D control the total granule number and the fraction of granules docked at the plasma membrane in PC12 cells

1 reference

12 December 2020

Changes of endoplasmic reticulum chaperone complexes, redox state, and impaired protein disulfide reductase activity in misfolding alpha1-antitrypsin transgenic mice

1 reference

12 December 2020

Intracellular inclusions containing mutant alpha1-antitrypsin Z are propagated in the absence of autophagic activity

1 reference

12 December 2020

Insights into checkpoint capacity

1 reference

12 December 2020

Hepatocyte Ultrastructural Changes in α1-Antitrypsin Deficiency

1 reference

12 December 2020

Ultrastructural Liver Pathology in Patients with Minimal Liver Disease and α1-Antitrypsin Deficiency: A Comparison Between Heterozygous and Homozygous Patients

1 reference

12 December 2020

Identifiers

DOI

10.1091/MBC.E07-06-0587

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:18045994%20AND%20SRC:MED&resulttype=core&format=json

28 December 2019

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:18045994%20AND%20SRC:MED&resulttype=core&format=json

28 December 2019

1 reference