Cyclophilin D, a target for counteracting skeletal muscle dysfunction in mitochondrial myopathy (Q36251975)

13 August 2017

Cyclophilin D, a target for counteracting skeletal muscle dysfunction in mitochondrial myopathy (English)

1 reference

13 August 2017

mitochondrial myopathy

1 reference

3

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:26374844%20AND%20SRC:MED&resulttype=core&format=json

2 June 2020

Arthur J Cheng

4

1 reference

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2 June 2020

Christoph Freyer

10

1 reference

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2 June 2020

Mattias Carlstrom

12

1 reference

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2 June 2020

Johanna T Lanner

13

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:26374844%20AND%20SRC:MED&resulttype=core&format=json

2 June 2020

Daniel C. Andersson

14

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:26374844%20AND%20SRC:MED&resulttype=core&format=json

2 June 2020

Anna Wredenberg

16

1 reference

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2 June 2020

Hakan Westerblad

17

1 reference

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2 June 2020

author name string

Charlotte Gineste

1

1 reference

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2 June 2020

Andres Hernandez

2

1 reference

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2 June 2020

Karin Naess

5

1 reference

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2 June 2020

Rolf Wibom

6

1 reference

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2 June 2020

Nicole Lesko

7

1 reference

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2 June 2020

Helene Bruhn

8

1 reference

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2 June 2020

Anna Wedell

9

1 reference

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2 June 2020

Shi-Jin Zhang

11

1 reference

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2 June 2020

Joseph D Bruton

15

1 reference

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2 June 2020

publication date

14 September 2015

1 reference

13 August 2017

Human Molecular Genetics

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:26374844%20AND%20SRC:MED&resulttype=core&format=json

2 June 2020

volume

24

1 reference

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2 June 2020

issue

23

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:26374844%20AND%20SRC:MED&resulttype=core&format=json

2 June 2020

page(s)

6580-6587

1 reference

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describes a project that uses

2 June 2020

ImageJ

1 reference

11 June 2022

https://www.ebi.ac.uk/europepmc/webservices/rest/PMC4634369/fullTextXML

inferred from PubMed Central ID database lookup

cites work

Distinct mPTP activation mechanisms in ischaemia-reperfusion: contributions of Ca2+, ROS, pH, and inorganic polyphosphate

1 reference

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The mitochondrial calcium uniporter complex: molecular components, structure and physiopathological implications

1 October 2017

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Calcineurin inhibitors: 40 years later, can't live without ...

1 October 2017

1 reference

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The physiological role of mitochondrial calcium revealed by mice lacking the mitochondrial calcium uniporter.

1 October 2017

1 reference

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Depressing mitochondria-reticulum interactions protects cardiomyocytes from lethal hypoxia-reoxygenation injury.

1 October 2017

1 reference

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The mitochondrial permeability transition pore: a mystery solved?

1 October 2017

1 reference

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Mitochondria as sensors and regulators of calcium signalling

1 October 2017

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A forty-kilodalton protein of the inner membrane is the mitochondrial calcium uniporter

1 October 2017

1 reference

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Integrative genomics identifies MCU as an essential component of the mitochondrial calcium uniporter

1 October 2017

1 reference

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MICU1 encodes a mitochondrial EF hand protein required for Ca(2+) uptake

1 October 2017

1 reference

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Cyclophilin D in mitochondrial pathophysiology

1 October 2017

1 reference

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The pathophysiology of mitochondrial disease as modeled in the mouse

1 October 2017

1 reference

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Cyclosporine A treatment for Ullrich congenital muscular dystrophy: a cellular study of mitochondrial dysfunction and its rescue

1 October 2017

1 reference

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Cyclosporin A corrects mitochondrial dysfunction and muscle apoptosis in patients with collagen VI myopathies

1 October 2017

1 reference

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Genetic and pharmacologic inhibition of mitochondrial-dependent necrosis attenuates muscular dystrophy

1 October 2017

1 reference

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Mitochondrial dysfunction in the pathogenesis of Ullrich congenital muscular dystrophy and prospective therapy with cyclosporins

1 October 2017

1 reference

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Chaperone-mediated coupling of endoplasmic reticulum and mitochondrial Ca2+ channels.

1 October 2017

1 reference

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Mitochondrial DNA mutations in human disease

1 October 2017

1 reference

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Calcium, ATP, and ROS: a mitochondrial love-hate triangle

1 October 2017

1 reference

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The ADP/ATP translocator is not essential for the mitochondrial permeability transition pore

1 October 2017

1 reference

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Increased mitochondrial mass in mitochondrial myopathy mice

1 October 2017

1 reference

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1 October 2017

Mitochondrial myopathies

1 reference

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Mitochondria and calcium: from cell signalling to cell death

1 October 2017

1 reference

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Oxygen-bridged dinuclear ruthenium amine complex specifically inhibits Ca2+ uptake into mitochondria in vitro and in situ in single cardiac myocytes

1 October 2017

1 reference

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Inhibition of Ca2(+)-induced large-amplitude swelling of liver and heart mitochondria by cyclosporin is probably caused by the inhibitor binding to mitochondrial-matrix peptidyl-prolyl cis-trans isomerase and preventing it interacting with the adeni

1 October 2017

1 reference

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Calcineurin is a common target of cyclophilin-cyclosporin A and FKBP-FK506 complexes

1 October 2017

1 reference

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Purification and N-terminal sequencing of peptidyl-prolyl cis-trans-isomerase from rat liver mitochondrial matrix reveals the existence of a distinct mitochondrial cyclophilin

1 October 2017

1 reference

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Mitochondrial disease heterogeneity: a prognostic challenge

1 October 2017

1 reference

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The cyclophilin inhibitor Debio 025 normalizes mitochondrial function, muscle apoptosis and ultrastructural defects in Col6a1-/- myopathic mice.

29 June 2018

1 reference

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Inhibition of the mitochondrial calcium uniporter by the oxo-bridged dinuclear ruthenium amine complex (Ru360) prevents from irreversible injury in postischemic rat heart

29 June 2018

1 reference

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Inhibition by cyclosporin A of a Ca2+-dependent pore in heart mitochondria activated by inorganic phosphate and oxidative stress

29 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4634369

Reconstitution in planar lipid bilayers of a voltage-dependent anion-selective channel obtained from paramecium mitochondria

29 June 2018

1 reference

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Genetic ablation of cyclophilin D rescues mitochondrial defects and prevents muscle apoptosis in collagen VI myopathic mice

29 June 2018

1 reference

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Increased mitochondrial Ca2+ and decreased sarcoplasmic reticulum Ca2+ in mitochondrial myopathy

22 September 2018

1 reference

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Mitochondrial dysfunction and apoptosis in myopathic mice with collagen VI deficiency.

22 September 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4634369

Measurement of ATP production and respiratory chain enzyme activities in mitochondria isolated from small muscle biopsy samples

22 September 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4634369

Cyclosporin A is a potent inhibitor of the inner membrane permeability transition in liver mitochondria

22 September 2018

1 reference

12 December 2020

Effect of hydrogen peroxide and dithiothreitol on contractile function of single skeletal muscle fibres from the mouse

1 reference

12 December 2020

Metabolic differentiation of distinct muscle types at the level of enzymatic organization

1 reference

12 December 2020

Mitochondrial cytopathies

1 reference

12 December 2020

Identifiers

DOI

10.1093/HMG/DDV361

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:26374844%20AND%20SRC:MED&resulttype=core&format=json

2 June 2020

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:26374844%20AND%20SRC:MED&resulttype=core&format=json

2 June 2020

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:26374844%20AND%20SRC:MED&resulttype=core&format=json