Effect of rapamycin on the fate of P23H opsin associated with retinitis pigmentosa (an American Ophthalmological Society thesis). (Q35662681)

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30 December 2019

title

Effect of rapamycin on the fate of P23H opsin associated with retinitis pigmentosa (an American Ophthalmological Society thesis) (English)

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30 December 2019

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1 reference

Shalesh Kaushal

1

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30 December 2019

publication date

1 January 2006

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Transactions of the American Ophthalmological Society annual meeting

30 December 2019

published in

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30 December 2019

volume

104

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30 December 2019

page(s)

517-529

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Rhodopsin maturation defects induce photoreceptor death by apoptosis: a fly model for RhodopsinPro23His human retinitis pigmentosa

30 December 2019

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The C-terminal region of an Apg7p/Cvt2p is required for homodimerization and is essential for its E1 activity and E1-E2 complex formation

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12 July 2018

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LC3, a mammalian homologue of yeast Apg8p, is localized in autophagosome membranes after processing

12 July 2018

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Description of a new mutation in rhodopsin, Pro23Ala, and comparison with electroretinographic and clinical characteristics of the Pro23His mutation

12 July 2018

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12 July 2018

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Lysosomal involvement in the removal of clofibrate-induced rat liver peroxisomes. A biochemical and morphological analysis.

12 July 2018

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Regulation of sorting and post-Golgi trafficking of rhodopsin by its C-terminal sequence QVS(A)PA.

12 July 2018

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12 July 2018

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Transgenic mice carrying the dominant rhodopsin mutation P347S: evidence for defective vectorial transport of rhodopsin to the outer segments

12 July 2018

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12 July 2018

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Apoptosis: final common pathway of photoreceptor death in rd, rds, and rhodopsin mutant mice

12 July 2018

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Apoptotic photoreceptor cell death in mouse models of retinitis pigmentosa

12 July 2018

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12 July 2018

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Constitutive activation of phototransduction by K296E opsin is not a cause of photoreceptor degeneration

12 July 2018

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12 July 2018

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12 July 2018

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12 July 2018

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12 July 2018

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12 July 2018

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12 July 2018

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ABCA4 mutations causing mislocalization are found frequently in patients with severe retinal dystrophies

25 September 2018

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25 September 2018

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25 September 2018

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A rhodopsin mutant linked to autosomal dominant retinitis pigmentosa is prone to aggregate and interacts with the ubiquitin proteasome system

25 September 2018

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Genetically engineered large animal model for studying cone photoreceptor survival and degeneration in retinitis pigmentosa

25 September 2018

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25 September 2018

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Defective intracellular transport and processing of CFTR is the molecular basis of most cystic fibrosis

25 September 2018

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Formation of autophagosomes during degradation of excess peroxisomes induced by administration of dioctyl phthalate

25 September 2018

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12 December 2020

A rhodopsin gene mutation responsible for autosomal dominant retinitis pigmentosa results in a protein that is defective in localization to the photoreceptor outer segment

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12 December 2020

Inhibition of peroxisomal degradation by 3-methyladenine (3MA) in primary cultures of rat hepatocytes

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12 December 2020

Photoreceptor autophagy: effects of light history on number and opsin content of degradative vacuoles

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12 December 2020

The Delta F508 mutation shortens the biochemical half-life of plasma membrane CFTR in polarized epithelial cells

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12 December 2020

Increased degradation in rat liver induced by antilipolytic agents: a model for studying autophagy and protein degradation in liver?

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12 December 2020

Identifiers

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30 December 2019

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