SOD1 targeted to the mitochondrial intermembrane space prevents motor neuropathy in the Sod1 knockout mouse (Q34438640)

2 August 2017

SOD1 targeted to the mitochondrial intermembrane space prevents motor neuropathy in the Sod1 knockout mouse (English)

1 reference

2 August 2017

0 references

Lindsey R Fischer

1

1 reference

2 August 2017

Anissa Igoudjil

2

1 reference

2 August 2017

Jordi Magrané

3

1 reference

2 August 2017

Yingjie Li

4

1 reference

2 August 2017

Jason M Hansen

5

1 reference

2 August 2017

Giovanni Manfredi

6

1 reference

2 August 2017

Jonathan D Glass

7

1 reference

2 August 2017

language of work or name

English

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publication date

14 November 2010

1 reference

2 August 2017

1 reference

2 August 2017

134

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2 August 2017

Pt 1

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2 August 2017

196-209

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describes a project that uses

2 August 2017

ImageJ

1 reference

11 June 2022

https://www.ebi.ac.uk/europepmc/webservices/rest/PMC3009841/fullTextXML

inferred from PubMed Central ID database lookup

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Conditional knockout of Mn superoxide dismutase in postnatal motor neurons reveals resistance to mitochondrial generated superoxide radicals

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6 July 2018

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6 July 2018

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6 July 2018

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6 July 2018

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A spectrophotometric assay for superoxide dismutase activities in crude tissue fractions

6 July 2018

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6 July 2018

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Blue native electrophoresis for isolation of membrane protein complexes in enzymatically active form

6 July 2018

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6 July 2018

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SOD-1 deletions in Caenorhabditis elegans alter the localization of intracellular reactive oxygen species and show molecular compensation

6 July 2018

1 reference

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Cyclic AMP produced inside mitochondria regulates oxidative phosphorylation

27 October 2018

1 reference

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The disulfide relay system of mitochondria is required for the biogenesis of mitochondrial Ccs1 and Sod1.

27 October 2018

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Selective vulnerability of motor neurons and dissociation of pre- and post-synaptic pathology at the neuromuscular junction in mouse models of spinal muscular atrophy

27 October 2018

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Multiprotein complexes of the survival of motor neuron protein SMN with Gemins traffic to neuronal processes and growth cones of motor neurons

27 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3009841

Mitochondrial thioredoxin-2 has a key role in determining tumor necrosis factor-alpha-induced reactive oxygen species generation, NF-kappaB activation, and apoptosis.

27 October 2018

1 reference

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The GTPase dMiro is required for axonal transport of mitochondria to Drosophila synapses.

27 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3009841

Mutant superoxide dismutase 1 forms aggregates in the brain mitochondrial matrix of amyotrophic lateral sclerosis mice.

27 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3009841

Toxicity of familial ALS-linked SOD1 mutants from selective recruitment to spinal mitochondria.

27 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3009841

Mutated human SOD1 causes dysfunction of oxidative phosphorylation in mitochondria of transgenic mice.

27 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3009841

Purification and determination of activity of mitochondrial cyanide-sensitive superoxide dismutase in rat tissue extract

27 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3009841

Mice lacking cytosolic copper/zinc superoxide dismutase display a distinctive motor axonopathy

27 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3009841

Superoxide-mediated cytotoxicity in superoxide dismutase-deficient fetal fibroblasts

27 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3009841

Neuromuscular transmission in amyotrophic lateral sclerosis.

27 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3009841

Quantitative axon terminal and end-plate morphology in amyotrophic lateral sclerosis.

27 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3009841

Denervation-induced skeletal muscle atrophy is associated with increased mitochondrial ROS production

27 October 2018

1 reference

12 December 2020

Deleterious role of superoxide dismutase in the mitochondrial intermembrane space

1 reference

12 December 2020

Comparative analysis of motoneuron loss and functional deficits in PMN mice: implications for human motoneuron disease

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12 December 2020

Amyotrophic lateral sclerosis is a distal axonopathy: evidence in mice and man

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12 December 2020

Mitochondrial superoxide simutase. Site of synthesis and intramitochondrial localization

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12 December 2020

A spectroscopic characterization of a monomeric analog of copper, zinc superoxide dismutase

1 reference

12 December 2020

A vector for expressing foreign genes in the brains and hearts of transgenic mice

1 reference

12 December 2020

Massive mitochondrial degeneration in motor neurons triggers the onset of amyotrophic lateral sclerosis in mice expressing a mutant SOD1

1 reference

12 December 2020

Coincident thresholds of mutant protein for paralytic disease and protein aggregation caused by restrictively expressed superoxide dismutase cDNA

1 reference

12 December 2020

Selective vulnerability and pruning of phasic motoneuron axons in motoneuron disease alleviated by CNTF

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12 December 2020

Complete dissociation of motor neuron death from motor dysfunction by Bax deletion in a mouse model of ALS

1 reference

12 December 2020

The coupling between disulphide status, metallation and dimer interface strength in Cu/Zn superoxide dismutase

1 reference

12 December 2020

Mitochondrial alterations in the spinal cord of patients with sporadic amyotrophic lateral sclerosis

1 reference

12 December 2020

Identifiers

DOI

10.1093/BRAIN/AWQ314

1 reference

2 August 2017

1 reference

2 August 2017

1 reference