Mutation-dependent polymorphism of Cu,Zn-superoxide dismutase aggregates in the familial form of amyotrophic lateral sclerosis (Q33559556)

28 July 2017

Mutation-dependent polymorphism of Cu,Zn-superoxide dismutase aggregates in the familial form of amyotrophic lateral sclerosis (English)

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amyotrophic lateral sclerosis

28 July 2017

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Yoshiaki Furukawa

1

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Koji Yamanaka

object named as

Koji Yamanaka

series ordinal

3

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author name string

Kumi Kaneko

series ordinal

2

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28 July 2017

Nobuyuki Nukina

series ordinal

4

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28 July 2017

language of work or name

English

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publication date

19 April 2010

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Journal of Biological Chemistry

28 July 2017

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28 July 2017

285

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28 July 2017

29

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28 July 2017

22221-22231

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describes a project that uses

28 July 2017

ImageJ

1 reference

11 June 2022

https://www.ebi.ac.uk/europepmc/webservices/rest/PMC2903422/fullTextXML

inferred from PubMed Central ID database lookup

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A common property of amyotrophic lateral sclerosis-associated variants: destabilization of the copper/zinc superoxide dismutase electrostatic loop

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Complete loss of post-translational modifications triggers fibrillar aggregation of SOD1 in the familial form of amyotrophic lateral sclerosis

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Common denominator of Cu/Zn superoxide dismutase mutants associated with amyotrophic lateral sclerosis: decreased stability of the apo state

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21 June 2018

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21 June 2018

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21 June 2018

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Amyotrophic lateral sclerosis mutations have the greatest destabilizing effect on the apo- and reduced form of SOD1, leading to unfolding and oxidative aggregation.

21 January 2018

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Copper-binding-site-null SOD1 causes ALS in transgenic mice: aggregates of non-native SOD1 delineate a common feature

21 January 2018

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Histological evidence of protein aggregation in mutant SOD1 transgenic mice and in amyotrophic lateral sclerosis neural tissues

21 January 2018

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Fibrillar inclusions and motor neuron degeneration in transgenic mice expressing superoxide dismutase 1 with a disrupted copper-binding site

21 January 2018

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Sequence and structural determinants of Cu, Zn superoxide dismutase aggregation

21 January 2018

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Somatodendritic accumulation of misfolded SOD1-L126Z in motor neurons mediates degeneration: alphaB-crystallin modulates aggregation

21 January 2018

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12 December 2020

Truncated wild-type SOD1 and FALS-linked mutant SOD1 cause neural cell death in the chick embryo spinal cord

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12 December 2020

Disulphide-reduced superoxide dismutase-1 in CNS of transgenic amyotrophic lateral sclerosis models

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12 December 2020

The coupling between disulphide status, metallation and dimer interface strength in Cu/Zn superoxide dismutase

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12 December 2020

Rats expressing human cytosolic copper-zinc superoxide dismutase transgenes with amyotrophic lateral sclerosis: associated mutations develop motor neuron disease

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12 December 2020

Fibril conformation as the basis of species- and strain-dependent seeding specificity of mammalian prion amyloids

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12 December 2020

Identifiers

DOI

10.1074/JBC.M110.113597

1 reference

28 July 2017

1 reference

28 July 2017

1 reference