LYRM7/MZM1L is a UQCRFS1 chaperone involved in the last steps of mitochondrial Complex III assembly in human cells (Q32884553)

11 July 2017

title

LYRM7/MZM1L is a UQCRFS1 chaperone involved in the last steps of mitochondrial Complex III assembly in human cells (English)

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Cytochrome c oxidase subunit I

11 July 2017

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Superoxide dismutase 2

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Ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1

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LYR motif containing 7

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ubiquinol-cytochrome c reductase core protein 2

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cellular respiration

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4

Massimo Zeviani

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11 July 2017

Ester Sánchez

1

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11 July 2017

Teresa Lobo

2

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11 July 2017

Jennifer L Fox

3

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11 July 2017

Dennis R Winge

5

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11 July 2017

Erika Fernández-Vizarra

6

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11 July 2017

language of work or name

English

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publication date

17 November 2012

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Biochimica et Biophysica Acta

11 July 2017

published in

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11 July 2017

volume

1827

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11 July 2017

issue

3

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11 July 2017

page(s)

285-293

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Late-stage maturation of the Rieske Fe/S protein: Mzm1 stabilizes Rip1 but does not facilitate its translocation by the AAA ATPase Bcs1

11 July 2017

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21 June 2018

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21 June 2018

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21 June 2018

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21 June 2018

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21 June 2018

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21 June 2018

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21 June 2018

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21 June 2018

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21 June 2018

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21 June 2018

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21 June 2018

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21 June 2018

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Impaired complex III assembly associated with BCS1L gene mutations in isolated mitochondrial encephalopathy

21 June 2018

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21 June 2018

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21 June 2018

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21 June 2018

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21 June 2018

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A mutant mitochondrial respiratory chain assembly protein causes complex III deficiency in patients with tubulopathy, encephalopathy and liver failure.

21 June 2018

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21 June 2018

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21 June 2018

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The mitochondrial targeting presequence of the Rieske iron-sulfur protein is processed in a single step after insertion into the cytochrome bc1 complex in mammals and retained as a subunit in the complex

21 June 2018

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21 June 2018

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21 June 2018

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12 December 2020

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Identifiers

DOI

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11 July 2017

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11 July 2017

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