Doppel-induced cerebellar degeneration in transgenic mice (Q24555049)

1

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P Mastrangelo

2

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E Bouzamondo

3

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C Heinrich

4

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G Legname

5

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L Hood

7

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D Westaway

8

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S J DeArmond

9

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P Tremblay

Proceedings of the National Academy of Sciences of the United States of America

10

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language of work or name

English

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publication date

18 December 2001

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published in

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volume

98

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issue

26

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page(s)

15288-93

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cites work

Two different neurodegenerative diseases caused by proteins with similar structures

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Expression and structural characterization of the recombinant human doppel protein

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Ataxia in prion protein (PrP)-deficient mice is associated with upregulation of the novel PrP-like protein doppel

24 March 2017

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Doppel is an N-glycosylated, glycosylphosphatidylinositol-anchored protein. Expression in testis and ectopic production in the brains of Prnp(0/0) mice predisposed to Purkinje cell loss

27 September 2017

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Mimicking dominant negative inhibition of prion replication through structure-based drug design

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COOH-terminal sequence of the cellular prion protein directs subcellular trafficking and controls conversion into the scrapie isoform

27 September 2017

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Long-range disruption of gene expression by a selectable marker cassette

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Prion isolate specified allotypic interactions between the cellular and scrapie prion proteins in congenic and transgenic mice

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Double replacement gene targeting for the production of a series of mouse strains with different prion protein gene alterations

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Heritable disorder resembling neuronal storage disease in mice expressing prion protein with deletion of an alpha-helix

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Antibodies to a scrapie prion protein.

30 May 2018

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Identification of prion amyloid filaments in scrapie-infected brain.

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Transgenic mice expressing hamster prion protein produce species-specific scrapie infectivity and amyloid plaques.

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Scrapie prion protein contains a phosphatidylinositol glycolipid

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Transgenetic studies implicate interactions between homologous PrP isoforms in scrapie prion replication.

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Normal development and behaviour of mice lacking the neuronal cell-surface PrP protein

30 May 2018

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129/Ola mice carrying a null mutation in PrP that abolishes mRNA production are developmentally normal.

30 May 2018

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Loss of cerebellar Purkinje cells in aged mice homozygous for a disrupted PrP gene.

21 January 2018

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Degeneration of skeletal muscle, peripheral nerves, and the central nervous system in transgenic mice overexpressing wild-type prion proteins

21 January 2018

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A C-terminal-truncated PrP Isoform Is Present in Mature Sperm

21 January 2018

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[Physiopathology and molecular diagnosis for prion diseases]

21 January 2018

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In vivo transfer of GPI-linked complement restriction factors from erythrocytes to the endothelium

28 November 2018

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PubMed

https://pubmed.ncbi.nlm.nih.gov/11734625

inferred from PubMed ID database lookup

12 December 2020

based on heuristic

The effects of formalin fixation on the detection of apoptosis in human brain by in situ end-labelling of DNA

1 reference

PubMed

https://pubmed.ncbi.nlm.nih.gov/11734625

inferred from PubMed ID database lookup

12 December 2020

based on heuristic

Quantitative trait loci affecting prion incubation time in mice

1 reference

PubMed

https://pubmed.ncbi.nlm.nih.gov/11734625

inferred from PubMed ID database lookup

12 December 2020

based on heuristic

Identifiers

DOI

10.1073/PNAS.251550798

1 reference

1376327

ADS bibcode

2001PNAS...9815288M

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1376327

1 reference

1 reference

1 reference