Altered status of glutathione and its metabolites in cystinotic cells (Q24305285)

glutathione metabolic process

GOA release 2020-03-11

1 reference

GOA release 2020-03-11

1 reference

Henk Blom

6

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ORCID Public Data File 2021

Elena Levtchenko

1

object named as

Elena Levtchenko

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Lambertus van den Heuvel

4

object named as

Lambertus van den Heuvel

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Martijn J Wilmer

3

object named as

Martijn Wilmer

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author name string

Adriana de Graaf-Hess

2

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Leo Monnens

Nephrology Dialysis Transplantation

5

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language of work or name

English

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publication date

September 2005

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published in

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volume

20

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issue

9

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page(s)

1828-32

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cites work

Severity of phenotype in cystinosis varies with mutations in the CTNS gene: predicted effect on the model of cystinosin

1 reference

https://api.crossref.org/works/10.1093%2FNDT%2FGFH932

The Fanconi syndrome of cystinosis: insights into the pathophysiology

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FNDT%2FGFH932

The physiological consequences of glutathione variations.

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FNDT%2FGFH932

Mitochondrial changes associated with glutathione deficiency

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FNDT%2FGFH932

Effect of glutathione depletion on sites and topology of superoxide and hydrogen peroxide production in mitochondria.

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FNDT%2FGFH932

Reversible glutathionylation of complex I increases mitochondrial superoxide formation

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FNDT%2FGFH932

Altered oxidative metabolism, motility, and adherence in phagocytic cells from cystinotic children

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FNDT%2FGFH932

Comparison of cystine determination in mixed leukocytes vs polymorphonuclear leukocytes for diagnosis of cystinosis and monitoring of cysteamine therapy

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FNDT%2FGFH932

Glutathione precursors replenish decreased glutathione pool in cystinotic cell lines

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FNDT%2FGFH932

Glutathione synthetase deficiency: is gamma-glutamylcysteine accumulation a way to cope with oxidative stress in cells with insufficient levels of glutathione?

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FNDT%2FGFH932

Mitochondrial free radical production and cell signaling

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FNDT%2FGFH932

Lysosomal cystine storage augments apoptosis in cultured human fibroblasts and renal tubular epithelial cells

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FNDT%2FGFH932

Cystine, cysteine, and glutathione metabolism in normal and cystinotic fibroblasts in vitro, and in cultured normal amniotic fluid cells

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FNDT%2FGFH932

7 January 2021

Glutathione in fibroblasts from normal and cystinotic children

1 reference

https://api.crossref.org/works/10.1093%2FNDT%2FGFH932

7 January 2021

Pyroglutamic aciduria and nephropathic cystinosis

1 reference

https://api.crossref.org/works/10.1093%2FNDT%2FGFH932

7 January 2021

Albumin turns on a vicious spiral of oxidative stress in renal proximal tubules

1 reference

https://api.crossref.org/works/10.1093%2FNDT%2FGFH932

7 January 2021