Crystallographic structure of human beta-hexosaminidase A: interpretation of Tay-Sachs mutations and loss of GM2 ganglioside hydrolysis (Q24602891)

2

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Maia M Cherney

3

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Stephen G Withers

4

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Don J Mahuran

5

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Michael N G James

Journal of Molecular Biology

6

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language of work or name

English

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publication date

16 June 2006

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published in

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volume

359

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page(s)

913-29

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issue

4

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GM1-ganglioside-mediated activation of the unfolded protein response causes neuronal death in a neurodegenerative gangliosidosis

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PROCHECK: a program to check the stereochemical quality of protein structures

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MOLREP: an Automated Program for Molecular Replacement

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Identifiers

DOI

10.1016/J.JMB.2006.04.004

1 reference

1837499

1837499

1 reference

1 reference

1 reference