Cooperation between COA6 and SCO2 in COX2 maturation during cytochrome c oxidase assembly links two mitochondrial cardiomyopathies (Q24337420)

plasma membrane ATP synthesis coupled electron transport

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Putative thioredoxin peroxidase SCO2 YBR024W

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Coa6p YMR244C-A

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Cytochrome c oxidase subunit 2 Q0250

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1 reference

9

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David Pacheu-Grau

object named as

David Pacheu-Grau

1

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author name string

Bettina Bareth

2

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Jan Dudek

3

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Lisa Juris

4

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F-Nora Vögtle

5

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Mirjam Wissel

6

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Scot C Leary

7

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Sven Dennerlein

8

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Markus Deckers

Cytochrome c oxidase deficiency

10

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language of work or name

English

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publication date

2 June 2015

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published in

Cell Metabolism

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volume

21

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page(s)

823-33

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issue

6

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cites work

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Rcf1 mediates cytochrome oxidase assembly and respirasome formation, revealing heterogeneity of the enzyme complex

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Oxa1p mediates the export of the N- and C-termini of pCoxII from the mitochondrial matrix to the intermembrane space

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Fatal infantile cardioencephalomyopathy with COX deficiency and mutations in SCO2, a COX assembly gene

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Inventory control: cytochrome c oxidase assembly regulates mitochondrial translation

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Human ERAL1 is a mitochondrial RNA chaperone involved in the assembly of the 28S small mitochondrial ribosomal subunit

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SCO1 and SCO2 act as high copy suppressors of a mitochondrial copper recruitment defect in Saccharomyces cerevisiae

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hCOA3 stabilizes cytochrome c oxidase 1 (COX1) and promotes cytochrome c oxidase assembly in human mitochondria.

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COX23, a homologue of COX17, is required for cytochrome oxidase assembly

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Human Sco1 and Sco2 function as copper-binding proteins

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